IgG4相关系统性疾病(IgG4-related systemic disease,IgG4-RSD)是一组最近认识的临床综合征,可累及多个器官,胰腺最常受累,主要表现为血清IgG4升高,受累组织弥漫IgG4阳性浆细胞浸润.本文主要介绍IgG4-RSD累及肾脏时的临床表现、影像学、实验室检查、病理特点及治疗情况.%IgG4-related systemic disease represents a recently recognized group of multi-organ diseases characterized by a high level of serum IgG4 and dense infiltration of IgG4-positive cells into multiple organs. The most commonly involved organ was pancreas. In this article,the relevant literatures about the renal involvements of IgG4-related systemic disease will be reviewed.
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