原发性葡萄膜淋巴瘤虽然也是眼内的淋巴瘤,但它的临床特征与原发性眼内(玻璃体视网膜)淋巴瘤完全不同,属于低度恶性B细胞型、粘膜相关性淋巴瘤.该病预后非常好,仅少数患者在治疗后发展为全身性病变,通常不侵犯中枢神经系统,但可蔓延至球结膜下或巩膜表层.本文报告1例确诊为原发性葡萄膜淋巴瘤、经过外放射治疗效果显著的病例,并对这种罕见疾病进行了文献复习.%Primary uveal lymphoma is a type of intra-ocular lymphoma. Unlike the intra-ocular lymphomas involving the retina and vitreous,primary uveal lymphoma generally has a low-grade nature and an indolent clinical course.It is a relatively rare condition,and the diagnosis can be challenging.We present a rare case of primary uveal lymphoma involving the choroid, ciliary body,iris and conjunctiva that was successfully treated with radiotherapy and achieved full remission.
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