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首页> 外文期刊>International Journal of Research in Medical Sciences >Klippel Trenaunay Weber syndrome with unilateral polycystic kidney disease: a rare presentation
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Klippel Trenaunay Weber syndrome with unilateral polycystic kidney disease: a rare presentation

机译：Klippel Trenaunay Weber综合征伴单侧多囊肾病：一种罕见的表现

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Klippel Trenaunay Weber syndrome (KTWS) is a rare disease characterized by hemihypertrophy, variceal enlargement of the veins, and arteriovenous (AV) malformations. Renal involvement in KTWS is not known except in rare case reports. Herein, we present a case of KTWS with unilateral polycystic kidney. A 52-year-old male was admitted due to pain left lumbar region for the last three months. The physical findings were increased diameter and increased length of the left leg compared with the right one, diffuse variceal enlargements on left leg, portwine stain on left side on neck, thorax, abdomen, left upper limb and left lower limb and a few hemangiomatous lesions on the left leg. Radiographic findings were cystic lesions in the left kidney, varicose veins in left leg, and hypertrophy of the soft tissues of the proximal left leg. Color Doppler of left lower limb showed incompetence of the saphenofemoral junction. He was diagnosed to have KTWS with these findings. Renal function tests of the patient were in the normal range. Patient's only complain was left lumbar region pain, mild in intensity. Patient was managed symptomatically.
机译：Klippel Trenaunay Weber综合征（KTWS）是一种罕见的疾病，其特征在于肥大，静脉曲张扩大和动静脉（AV）畸形。除极少数病例报告外，尚无肾脏参与KTWS的报道。在这里，我们介绍了单侧多囊肾的KTWS病例。最近三个月，一名52岁男性因腰椎左侧疼痛而入院。体格检查结果为：与右腿相比，左腿直径增加，长度增加，左腿弥漫性静脉曲张扩大，颈部左侧左侧，左侧，左侧，左侧，左侧，左侧，左侧，左侧，左侧，左侧，左侧，右侧，左侧，左侧，右侧，左侧，右侧，左侧，右侧，左侧，右侧，右侧，右侧，右侧，右侧，右侧，右侧，右侧，右侧，右侧，右侧，右侧，右侧，右侧，右侧，右侧，右侧，右侧，右侧，右侧，右侧，右侧和右侧的血管瘤。在左腿上。影像学检查结果为左肾的囊性病变，左腿的静脉曲张以及左腿近端的软组织肥大。左下肢彩色多普勒显示隐股交界处无功能。这些发现被诊断为患有KTWS。患者的肾功能检查在正常范围内。患者唯一的抱怨是左腰部疼痛，强度轻。对症治疗。

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