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首页> 外文期刊>Oncology, Gastroenterology and Hepatology Reports >Infantile hepatic hemangioendothelioma in an 11?year?old child: A case report and review of literature
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Infantile hepatic hemangioendothelioma in an 11?year?old child: A case report and review of literature

机译：一名11岁儿童的小儿肝血管内皮瘤：一例病例报告并文献复习

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Infantile hepatic hemangioendothelioma (IHH) is a rare benign mesenchymal tumor. As the name implies, it is commonly seen in infancy and has variable clinical presentation and outcome. This tumor can spontaneously regress or can have expansile growth replacing whole of the liver. In very large tumors, there may be extensive arteriovenous shunting within the lesion, resulting congestive heart failure (CHF) in a significant number of patients with poor outcome. Since there is no tumor marker for this tumor, the diagnosis can only be suspected on the basis of clinical features and radiological investigations from among the various mass occupying lesions of the liver in this age group, which includes hepatoblastoma, mesenchymal hamartoma or hepatocellular carcinoma. As a result, the management strategy cannot be defined and in the literature also there are isolated reports with diverse treatment protocols. The medical management includes corticosteroid, interferon, cytotoxic agents and irradiation or even the radical interventions such as hepatic artery ligation, transcatheter hepatic artery embolization. The surgical options are biopsy, complete resection of the lesion or even liver transplantation. We are reporting a case of IHH who was managed with surgical resection and postoperative corticosteroid. However, the patient had recurrence of the tumor and developed CHF, which led to the demise of the patient. The idea of reporting this case is that this patient was 11?year?old child who very unusual for this tumor at this age, and the surgical resection of this lesion should be radical rather than just excision biopsy as was done in the present case.
机译：婴儿肝血管内皮瘤（IHH）是一种罕见的良性间质肿瘤。顾名思义，它在婴儿期很常见，临床表现和预后也各不相同。该肿瘤可自发消退或可发生膨胀性增长，从而取代了整个肝脏。在非常大的肿瘤中，病变内可能会发生广泛的动静脉分流，从而导致大量不良预后的患者出现充血性心力衰竭（CHF）。由于没有针对该肿瘤的肿瘤标志物，因此只能根据临床特征和影像学检查怀疑该年龄组肝脏的各种占位性病变，包括肝母细胞瘤，间充质错构瘤或肝细胞癌。结果，不能定义管理策略，并且在文献中也存在具有不同治疗方案的孤立报告。医疗管理包括皮质类固醇，干扰素，细胞毒剂和辐射，甚至进行根本性干预，例如肝动脉结扎，经导管肝动脉栓塞。手术选择是活检，病变完全切除甚至肝移植。我们正在报告一例IHH，该患者经手术切除和术后糖皮质激素治疗。然而，患者复发肿瘤并发展为CHF，这导致患者死亡。报告此病例的想法是，该患者是11岁的孩子，在这个年龄段该肿瘤非常罕见，因此，对该病变的手术切除应该是根治性的，而不仅仅是本例中的切除活检。

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