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首页> 外文期刊>Journal of Clinical and Diagnostic Research >Mesenteric Fibromatosis (Desmoid Tumour) - A Rare Case Report
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Mesenteric Fibromatosis (Desmoid Tumour) - A Rare Case Report

机译：肠系膜纤维瘤病（胶质瘤）-罕见病例报告

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Mesenteric Fibromatosis (MF) is a proliferative fibroblastic lesion of small intestinal mesentery. It constitutes 8% of all desmoid tumours, which represent 0.03% of all neoplasm. It is histologically benign but may invade locally and recur after excision. It occurs sporadically or in association with Familial adenomatous polyposis (FAP) mutation as a component of Gardner?s syndrome. The presenting features of MF are asymptomatic abdominal mass, abdominal discomfort or pain, bowel or ureteral obstruction, intestinal perforation, fistula, functional impairment of ileoanal anastomosis following colectomy in FAP cases. A 29-year-old male presented with a swelling on the right side of the umbilicus for six months and dull aching pain for two months. Fine needle aspiration cytology, ultrasonography, contrast enhanced computerized tomography findings were inconclusive. After Exploratory laparotomy, a mass approx 6x5x4 cm in ileal mesentery was identified and excised along with 20cm of ileum. End to end anastomosis was done and specimen was sent for histopathology which confirmed the diagnosis of MF. Considering the rarity of this tumour and difficulties in diagnostic and therapeutic ambit, we believe it is justified to describe this case which came to our observation.
机译：肠系膜纤维瘤病（MF）是小肠系膜的增生性纤维母细胞病变。它占所有胶质瘤的8％，占所有肿瘤的0.03％。它在组织学上是良性的，但可能会局部侵袭并在切除后复发。它偶尔或与家族性腺瘤性息肉病（FAP）突变一起发生，作为Gardner's综合征的一部分。 MF的表现为无症状腹部肿块，腹部不适或疼痛，肠或输尿管阻塞，肠穿孔，瘘管，FAP病例结肠切除术后回肠吻合口功能受损。一名29岁的男性在脐带右侧出现肿胀六个月，并在两个月内出现了钝痛。细针穿刺细胞学检查，超声检查，对比增强的计算机断层扫描结果尚无定论。探索性剖腹手术后，在回肠系膜中发现约6x5x4 cm的肿块，并与20cm的回肠一起切除。进行了端到端吻合，并将标本送去进行组织病理学检查，证实了MF的诊断。考虑到这种肿瘤的稀有性以及诊断和治疗领域的困难，我们认为描述这种情况是合理的。

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