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首页> 外文期刊>Journal of Clinical and Diagnostic Research >Idiopathic Systemic Capillary Leak Syndrome: A Diagnostic Challengeand Its Management OD01-OD02
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Idiopathic Systemic Capillary Leak Syndrome: A Diagnostic Challengeand Its Management OD01-OD02

机译:特发性系统性毛细血管渗漏综合征:诊断挑战及其管理OD01-OD02

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Idiopathic Systemic Capillary Leak Syndrome (ISCLS) is a fatal disorder characterised by recurrent episodes of hypotension, hypoalbuminemia and haemoconcentration. It is a rare disease, underreported partly because of unawareness of treating physician. Here is a description of a 30 year old male presenting with history of fever, generalized oedema progressing to hypovolemic shock and multi organ dysfunction. His laboratory studies showed haemoconcenration, hypoalbuminemia and monoclonal gammopathy with negative bacteriological cultures. After excluding other probable etiologies he was diagnosed to have ISCLS. He was managed successfully with intravenous methylprednisolone, theophylline and other supportive measures. He has been put on prophylactic oral theophylline for one year.
机译:特发性系统性毛细血管泄漏综合症(ISCLS)是一种致命疾病,其特征是反复出现低血压,低白蛋白血症和血液浓缩。它是一种罕见疾病,漏报的部分原因是不了解治疗医师。这是对一名30岁男性的描述,该男性有发烧史,广泛性水肿发展为低血容量性休克和多器官功能障碍。他的实验室研究显示血液浓缩,低蛋白血症和细菌性培养阴性的单克隆丙种球蛋白病。排除其他可能的病因后,他被诊断患有ISCLS。通过静脉注射甲基强的松龙,茶碱和其他支持性措施成功治疗了他。他已经接受了预防性口服茶碱治疗一年。

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