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机译:Functional genomics and biochemical characterization of the C-elegans orthologue of the Machado-Joseph disease protein ataxin-3
Univ Minho, Life & Hlth Sci Res Inst, Hlth Sci Sch, P-4710057 Braga, Portugal;
Univ Calif Los Angeles, Program Neurogenet, Dept Neurol, David Geffen Sch Med, Los Angeles, CA USA;
UnIGENe, Inst Mol & Cell Biol, Oporto, PortugalUniv Utah, Dept Biol, Salt Lake City, UT 84112 USA;
polyglutamine disorders; ubiquitin-proteasome pathway; microarray; ataxia; knockout; VALOSIN-CONTAINING PROTEIN; CAENORHABDITIS-ELEGANS; NEUROLOGICAL DISEASE; RNA INTERFERENCE; AZORES ISLANDS; GENE-PRODUCT; F-BOX; EXPRESSION; LOCALIZATION; PROTEOLYSIS;