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首页> 外文期刊>Case Reports in Cardiology >Biventricular Noncompaction Cardiomyopathy in a Patient Presenting with New Onset Seizure: Case Report
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Biventricular Noncompaction Cardiomyopathy in a Patient Presenting with New Onset Seizure: Case Report

机译:发作新发作的患者的双室非致密性心肌病:病例报告

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摘要

Ventricular noncompaction (VNC) of the myocardium is a rare genetic cardiomyopathy caused by a disorder during endocardial morphogenesis and could be accompanied by life-threatening complications. The major clinical manifestations of VNC are heart failure, arrhythmias, and embolic events. The left ventricle is the most commonly reported affected site, but a few cases of right ventricular involvement have also been reported. We report a case of biventricular noncompaction cardiomyopathy in a 31-year-old woman presenting with a new onset seizure. On the second day of her telemetry-monitored hospitalization, she suffered a witnessed ventricular fibrillation arrest requiring emergency direct-current cardioversion and induced hypothermia. Transthoracic echocardiography (TTE) showed isolated left ventricular (LV) noncompaction and depressed LV systolic function. Subsequent cardiac magnetic resonance imaging (MRI) revealed both left and right ventricular noncompaction. This unusual presentation highlights the importance of a complete and thorough evaluation of patients even when presenting with apparently noncardiac symptom(s).
机译:心肌的心室非紧致性(VNC)是一种罕见的遗传性心肌病,由心内膜形态发生过程中的疾病引起,并可能伴有危及生命的并发症。 VNC的主要临床表现是心力衰竭,心律不齐和栓塞事件。左心室是最常报告的受累部位,但也有几例右心室受累的病例。我们报道了一名31岁的妇女出现新的发作性癫痫的双心室非紧致型心肌病。在进行遥测监测的住院的第二天,她目击了心室纤颤,需要紧急直流电复律并诱发体温过低。经胸超声心动图(TTE)显示孤立的左心室(LV)不紧密和左室收缩功能降低。随后的心脏磁共振成像(MRI)显示左心室和右心室均不紧密。这种不寻常的表现突出显示了即使表现出明显的非心脏症状也必须对患者进行全面而彻底的评估的重要性。

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