Choroid plexus papilloma (CPP) is a benign tumor of neuroectodermal origin that occurs most commonly in the posterior fossa of adults [5]. Complete resection of the tumor typically results in a cure, but intracranial and spinal drop metastases occur [5, 8]. We present a patient with intracranial metastases from CPP involving both cerebel-lopontine angles (CPAs) and mimicking neurofibromatosis type 2 (NF2) [4]. When a 35 year old patient complained of headaches and episodes of blurred vision, an MRI scan was performed and revealed a well-circumscribed, contrast-enhancing, midline lesion in the fourth ventricle with no hydroceph-alus. Suboccipital craniectomy resulted in macroscopically total excision of a well-circumscribed CPP. Sixteen years later, he developed transient visual obscurations in both eyes. Visual acuity was modestly reduced, left more than right, with a 2+ afferent pupillary defect on the left and moderate atrophic papilledema bilaterally. Hearing was decreased on the left; he had no cafe au lait spots or other skin lesions.
展开▼
