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首页> 外文期刊>Pediatric dermatology >Diffuse Capillary Malformation in Association with Fetal Pleural Effusion: Report of Five Patients
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Diffuse Capillary Malformation in Association with Fetal Pleural Effusion: Report of Five Patients

机译：弥漫性毛细血管畸形伴胎儿胸腔积液：五例报告

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摘要

Capillary malformation (CM) can be a "red flag" for several syndromic vascular anomalies. We identified a subset of patients with diffuse CM and fetal pleural effusion and documented the type of CM, the etiology of the pleural effusion, the potential syndromic diagnosis, and outcome. Patients with a history of CM and fetal pleural effusion were identified by searching the database of patients evaluated at the Vascular Anomalies Center at Boston Children's Hospital. Standardized patient interviews and a retrospective review of records, photographs, and imaging studies were conducted. Five patients had diffuse CM and fetal pleural effusion. Two patients had macrocephaly-CM (M-CM), one had features of M-CM and CLOVES (congenital lipomatous overgrowth, vascular malformations, epidermal nevi, and spinal/skeletal anomalies and/or scoliosis), and one had diffuse CM with overgrowth. The pleural fluid was chylous in four patients. One patient had thoracic lymphatic malformation. Recurrent effusion occurred in one patient coincident with pneumonia at age 11 years. Four patients had a history of reactive airway disease and episodic pulmonary infections. The diagnosis of vascular anomaly-overgrowth syndromes, particularly M-CM, should be considered in neonates with fetal pleural effusion.
机译：毛细血管畸形（CM）可能是一些综合征血管异常的“危险信号”。我们确定了弥漫性CM和胎儿胸腔积液的一部分患者，并记录了CM的类型，胸腔积液的病因，潜在的症状诊断和结局。通过搜索在波士顿儿童医院血管异常中心评估的患者数据库，鉴定出具有CM和胎儿胸腔积液病史的患者。进行了标准化的患者访谈以及对记录，照片和影像学研究的回顾性审查。 5例患者出现弥漫性CM和胎儿胸腔积液。两名患者患有大头型CM（M-CM），一名具有M-CM和CLOVES的特征（先天性脂肪瘤过度生长，血管畸形，表皮痣，脊柱/骨骼异常和/或脊柱侧弯），另一名患有弥漫性CM和过度生长。四名患者胸膜液呈乳白色。 1例患者有胸淋巴畸形。一名11岁的肺炎患者经常出现积液。 4例患者有反应性气道疾病和发作性肺部感染的病史。胎儿胸腔积液的新生儿应考虑诊断血管异常过度生长综合征，尤其是M-CM。

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