We present a case of aggressive angiomyxoma of the vulva. The patient presented with a persistent, enlarging vulvar mass, initially misdiagnosed as a Bartholin gland cyst. The patient underwent wide local excision, which resulted in total resection of the mass. Final pathology was consistent with aggressive angiomyxoma, a rare soft tissue tumor with a predilection for the female pelvis. Though rare, it is important to consider in the differential diagnosis of a pelvic mass, given the locally aggressive nature of this tumor and propensity for recurrence. Highlights ? Aggressive angiomyxoma is a rare soft tissue tumor occurring in the pelvic region of females. ? Differential diagnosis for a persistent vulvar mass should include consideration of this tumor. ? Gynecologic oncologists may manage these tumors due to propensity for deep invasion.
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