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首页> 外文期刊>Journal of Medical Case Reports >Isolated angioedema of the bowel due to C1 esterase inhibitor deficiency: a case report and review of literature
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Isolated angioedema of the bowel due to C1 esterase inhibitor deficiency: a case report and review of literature

机译：C1酯酶抑制剂缺乏引起的肠道孤立性血管性水肿：一例病例报告并文献复习

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Introduction We report a rare, classic case of isolated angioedema of the bowel due to C1-esterase inhibitor deficiency. It is a rare presentation and very few cases have been reported worldwide. Angioedema has been classified into three categories. Case presentation A 66-year-old Caucasian man presented with a ten-month history of episodic severe cramping abdominal pain, associated with loose stools. A colonoscopy performed during an acute attack revealed nonspecific colitis. Computed tomography of the abdomen performed at the same time showed a thickened small bowel and ascending colon with a moderate amount of free fluid in the abdomen. Levels of C4 (< 8 mg/dL; reference range 15 to 50 mg/dL), CH50 (< 10 U/mL; reference range 29 to 45 U/ml) and C1 inhibitor (< 4 mg/dL; reference range 14 to 30 mg/dL) were all low, supporting a diagnosis of acquired angioedema with isolated bowel involvement. Our patient's symptoms improved with antihistamine and supportive treatment. Conclusion In addition to a detailed comprehensive medical history, laboratory data and imaging studies are required to confirm a diagnosis of angioedema due to C1 esterase inhibitor deficiency.
机译：引言我们报告了由于C1酯酶抑制剂缺乏引起的罕见的经典孤立性肠血管性水肿病例。这是一次罕见的演讲，全世界鲜有报道。血管性水肿已分为三类。病例介绍一名66岁的白人男子，有10个月的发作性严重痉挛性腹痛病史，伴有稀便。急性发作期间进行的结肠镜检查显示非特异性结肠炎。同时进行的腹部计算机断层扫描显示，小肠增厚，结肠上升，腹部中有少量游离液。 C4（<8 mg / dL;参考范围15至50 mg / dL），CH50（<10 U / mL;参考范围29至45 U / ml）和C1抑制剂（<4 mg / dL;参考范围14）的水平至30 mg / dL）均偏低，支持诊断为孤立性肠受累后天性血管性水肿。抗组胺药和支持治疗可改善患者的症状。结论除了详细的综合病史之外，还需要实验室数据和影像学研究来证实由C1酯酶抑制剂缺乏引起的血管性水肿的诊断。

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