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首页> 外文期刊>The Canadian Journal of Neurological Sciences: le Journal Canadien des Sciences Neurologiques >P.052 Benign spasms of infancy - a mimicker of infantile epileptic disorders
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P.052 Benign spasms of infancy - a mimicker of infantile epileptic disorders

机译：P.052营养症良性痉挛 - 婴儿癫痫疾病的模仿者

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Background: Benign spasms of infancy (BSI), previously described as benign non-epileptic infantile spasms or benign myoclonus of early infancy, are non-epileptic movements manifesting during the first year of life and spontaneously resolving in the second year of life. BSI are characterized by spasms typically lasting 1-2 seconds, involving to varying degrees the head, neck, trunk, shoulders and upper extremities. Ictal and interictal EEG recordings are normal. BSI are not associated with developmental retardation and do not require treatment. Distinction between BSI and infantile epileptic disorders, such as epileptic spasms or myoclonic epilepsy of infancy, can be challenging given the clinical similarities. Moreover, interictal EEGs can be normal in all conditions. Epileptic spasms and myoclonic epilepsy require timely treatment to improve neurodevelopmental outcomes. Methods: We describe a 6-month old infant presenting with spasm-like movements. His paroxysms as well as a positive family history for epileptic spasms were in keeping with a likely diagnosis of West syndrome. Results: Surprisingly, ictal video EEG did not reveal epileptiform activity, and suggested a diagnosis of BSI. Conclusions: We emphasize that ictal EEG is the gold standard for classification of infantile paroxysms as either epileptic or non-epileptic, thereby avoiding overtreatment of BSI and facilitating timely targeted treatment of infantile epilepsies.
机译：背景：婴儿期（BSI）的良性痉挛，以前被描述为患有早期婴儿期良性的非癫痫婴儿痉挛或良性肌阵挛，是在生命的第一年和自发解决生命的第二年中的非癫痫发势。 BSI的特征在于通常持续1-2秒的痉挛，涉及变化的头部，颈部，躯干，肩部和上肢。 ICTAL和INTERINTAL EEG录音是正常的。 BSI与发育延迟无关，不需要治疗。鉴于临床相似之处，BSI和婴儿癫痫疾病（如癫痫痉挛或婴儿疾病的癫痫患者）的区别可能是挑战。此外，在所有条件下，嵌入脑电图都可以是正常的。癫痫痉挛和肌阵挛性癫痫需要及时治疗以改善神经发作的结果。方法：我们描述了一个6个月大的婴儿，呈现出痉挛的运动。他的阵发和癫痫痉挛的阳性家族史正在与西综合征的可能诊断保持一致。结果：令人惊讶的是，ICTAL视频EEG没有揭示癫痫型活性，并表明BSI的诊断。结论：我们强调ICTAL eeg是癫痫患者分类为癫痫或非癫痫的婴儿阵发性的金标准，从而避免了BSI的过度处理，并促进对婴儿癫痫的及时靶向治疗。

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